Pdf a midline nasopharyngeal heterotopic neuroglial tissue. Glial heterotopia is a rare nonhereditary, benign congenital malformation, which is composed of normal glial tissue isolated from the central nervous system. Interestingly, we demonstrated 17 a similar disruption of radial glial cells in. Ten cases of nasal glial heterotopic diagnosed between 1970 and. Glial heterotopia of the scalp in an infant singh apsp. To check the main types of gray matter heterotopia, common malformations of cortical. A rare presentation article pdf available in bmc ophthalmology 111. This is a pdf file of an unedited manuscript that has been. Heterotopic definition is occurring in an abnormal place. Glial periorbital heterotopia di pasquo journal of. Journal of pediatric ophthalmology and strabismus the authors describe a 5yearold boy who had three congenital anomalies clinical anophthalmos, meningocele, and glial heterotopia in the orbit. Bickler sw, glial heterotopia of the oral cavity, journal of pediatric surgery case reports 2015, doi. Nasal glial heterotopia nasal glioma is the name used to describe a mass composed of mature brain tissue isolated from the cranial cavity or spinal canal. We present a rare case of glial choristoma of the middle ear, together.
Heterotopia definition, misplacement or displacement, as of an organ. In this paper we report a midline glial heterotopia, which presented with upper airway obstruction in a newborn. Heterotopic brain tissue is very uncommon in the middle ear and mastoid. Nasal glioma is the most frequently encountered entity among congenital nasal masses, which are seen in one in 20,00040,000 live births. However, it must be considered in the differential diagnosis of airway obstruction in the newborn. Nasal glial heterotopia, also known as nasal glioma, is a rare developmental anomaly of the nasal cavity occurring in patients over a wide range of ages, with a predilection for presentation at birth or in early childhood. A wide variety of lesions, including malignant and benign tumors, may develop around the orbit. A2month old boy was evaluated for a subcutaneous mass on the right dorsum of his nose. The patient presented with an external pedunculated oral mass which was connected to the anterior hard palate by a firm, rubbery stalk of mucosal tissue. Glial heterotopia should also be considered for the differential diagnosis. Glial heterotopia or the occurrence of isolated non teratomatous extracranial glial tissue is rare. Pdf glial heterotopia of the middle ear researchgate.
Heterotopic neuroglial tissue is defined as a mass composed of mature brain tissue isolated from the cranial cavity or spinal canal. Nasal glial heterotopias ngh are rare nonhereditary congenital malformations composed of heterotopic neuroglial tissue. Counseling for the prognosis and postnatal treatment depends on antenatal suspicion. A choristoma is the presence of histologically normal tissue in an area where it is not normally located. Neuroglial ectopia has been defined as a mass composed of differentiated neuroectodermal tissue isolated from the spinal canal or cranial cavity and remains rare. Glial heterotopia is a nonneoplastic, extracranial midline malformation. It consists of differentiated neuroectodermal tissue outside the central nervous system. Pdf nasal glial heterotopia also known as nasal glioma, is a rare. We report a neonate with extensive extranasal glial heterotopia involving the left buccopharyngeal region, palate and. Neuroglial heterotopia, heterotopic brain tissue, or differentiated neural tissue outside the cranial vault is uncommon, and these anomalies most commonly occur in the nasal cavity.
Heterotopia definition of heterotopia by medical dictionary. Heterotopia definition of heterotopia by the free dictionary. Clinicians may commonly consider adenoid hypertrophy as the cause for the. Lu,sterzi,detit abstract achoristomaisthepresenceofhistologicallynormaltissueinanareawhereitisnotnormallylocated. Click here to submit manuscripts on our new open journal system. Heterotopic definition of heterotopic by merriamwebster. Glial heterotopia of the middle ear the journal of. Nasopharyngeal glial heterotopia with intracranial.
The most frequently reported choristoma of the middle ear is salivary choristoma. Differentiation of this lesion from nasal glioma and encephalocele is important. Not a true neoplasm but a malformation that cause tumorlike conditions in newborns and older infants. We report an unusual case of a glial heterotopia arising from the oral cavity of an african neonate.
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